Neuro-fibromatosis of the tongue in a child : together with a note on the classification of incomplete and anomalous cases of Recklinghausen's disease / by F. Parkes Weber.

  • Weber, Frederick Parkes, 1863-1962.
Date:
[1910]
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Licence: In copyright

Credit: Neuro-fibromatosis of the tongue in a child : together with a note on the classification of incomplete and anomalous cases of Recklinghausen's disease / by F. Parkes Weber. Source: Wellcome Collection.

Provider: This material has been provided by The Royal College of Surgeons of England. The original may be consulted at The Royal College of Surgeons of England.

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    and the general health of the boy appeared satisfactory in spite of his somewhat delicate appearance. The projecting portion of the tumour was kindly removed for me by Dr. Pfister; and Dr. J. C. G. Ledingliam, to whom I am much indebted, kindly examined it microscopically. Sections (see Fig. 2) showed bundles of medullated nerve-fibres bound together by a close connective-tissue stroma. The tumour was evidently neuro-fibro- matous, and a hard cord still remains to the right of the boy’s frasnum linguae, doubtless representing part of the lingual branch of the fifth cranial nerve. Fig. 2.—Microscopic section of a portion of the tumour, showing medullated nerve- fibres. I regard the tumour as a mild form of plexiform neuroma involv- ing one side of the tongue; in fact, I believe the condition to be a lesser degree of the “macroglossia (or rather hemi-macroglossia) neuro- fibromatosa” described by Abbott and Shattock in 1903,* and by Spencer and Shattock in 1907.t The case is, therefore, according to my classification, likewise to be considered as an (at least as yet) incomplete form of Recklinghausen’s disease, and in this connection it is interesting to note that there is a somewhat irregularly shaped cafe au lait patch of cutaneous pigmentation, occupying an area of three or four square inches, on the upper part of the front of the * Abbott and Shattock, ‘Trans. Path. Soc., Lond./ 1903, vol. liv, p. 231. f Spencer and Shattock, ‘ Proc. Roy. Soc. Med./ Pathological Section, 1908, vol. i, p. 8.